Sohanian Shabnam, Seifi Safoura, Kouchak Dezfouli Mohammad, Kiani Marjan, Khakbaz Oveys, Non-Syndromic Multiple Keratocystic Odontogenic Tumor: A Case Report, Journal of Otolaryngology Advances, Volume 2, Issue 1, 2017, Pages 7-11, ISSN 2379-8572, https://doi.org/10.14302/issn.2379-8572.joa-17-1668. (https://oap-researcharticles.org/joa/article/568) Abstract: A Keratocystic Odontogenic Tumor (KCOT) is a benign odontogenic lesion that is well-known for its histopathological features and invasive clinical behaviors. KCOTs may be non-syndromic or syndromic, and the syndromic type presents a higher risk of recurrence and invasive behaviors. Non-syndromic KCOTs are uncommon and account for only 5% of the cases. The purpose of the present case report is to conduct clinical, radiographic and pathologic evaluations and treat a 37-year-old man with non-syndromic nevoid basal cell carcinoma. Syndromic and non-syndromic keratocysts present more invasive behaviors than the solitary type. The initial symptoms of syndromic keratocysts appear as multiple keratocysts of the mandible and maxilla that are diagnosed by a dentist; as a result, the diagnosis and treatment of the disease is very crucial. Keywords: KCOT; basal cell nevus syndrome; syndromic; non-syndromic